Otosclerosis occurs when abnormal new bone forms in the inner ear. This growth prevents proper functioning of other ear structures. This condition is a common cause of hearing loss.
The Inner Ear
The cause of otosclerosis is still unknown. However, otosclerosis tends to run in families, and may be hereditary. Otosclerosis has also been linked to hormonal changes, especially pregnancy, and viral infections.
A risk factor is something that increases your chance of getting a disease or condition. Risk factors for otosclerosis include:
- Age: late teens through late 40s
- Family history of otosclerosis
- Sex: female
- Race: Caucasian or Asian
- Drinking nonfluoridated water: Some studies suggest that nonfluoridated water may cause a susceptible person to develop otosclerosis
- Pregnancy: may accelerate symptoms
Gradual hearing loss is the main symptom of otosclerosis. Hearing loss may be of two types:
- Conductive—involving the small bones of the inner ear
Sensorineural—involving the following structures:
- Cochlea—the sensory organ in the inner ear
- The major nerve pathway (8th cranial nerve) and/or area of the brain responsible for hearing
Early in the disease, you may first notice trouble hearing low-pitched sounds or whispers. Other symptoms may include:
- Balance problems
- Tinnitus]]> or sensation of ringing, roaring, or buzzing in the ear
The doctor will ask about your symptoms and medical history, and perform a physical exam. Tests may include:
- Hearing tests by an audiologist
- CT scan]]> —a type of x-ray that uses a computer to make pictures of the inside of the ear and head
- Examination of the middle ear at the time of surgery
Treatments may include:
Hearing aids may be effective for conductive and sensorineural hearing loss.
In many cases, a procedure called a stapedectomy may improve hearing. The purpose of this operation is to replace the diseased bone with an artificial device that can transmit sound waves to the inner ear. Stapedectomy is very effective and frequently returns hearing to a near normal level.
Fluoride tablets are sometimes prescribed to stabilize the condition and prevent further sensorineural hearing loss. However, this treatment remains controversial and unproven.
American Academy of Audiology
American Academy of Otolaryngology–Head and Neck Surgery
American Speech-Language-Hearing Association
Canadian Family Physician
Canadian Society of Otolaryngology
Department of Otolaryngology-Head and Neck Surgery, Northwestern University Medical School website. Available at: http://www.oto-hns.northwestern.edu/ .
National Institute on Deafness and Other Communication Disorders (NIDCD), National Institutes of Health website. Available at: http://www.nidcd.nih.gov/ .
Last reviewed November 2008 by ]]>Elie Edmond Rebeiz, MD, FACS]]>
Please be aware that this information is provided to supplement the care provided by your physician. It is neither intended nor implied to be a substitute for professional medical advice. CALL YOUR HEALTHCARE PROVIDER IMMEDIATELY IF YOU THINK YOU MAY HAVE A MEDICAL EMERGENCY. Always seek the advice of your physician or other qualified health provider prior to starting any new treatment or with any questions you may have regarding a medical condition.
Copyright © 2007 EBSCO Publishing All rights reserved.